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常染色体显性遗传性多囊肾病肾移植临床技术操作规范(2022版)

中华医学会器官移植学分会. 常染色体显性遗传性多囊肾病肾移植临床技术操作规范(2022版)[J]. 器官移植, 2023, 14(1): 24-30. doi: 10.3969/j.issn.1674-7445.2023.01.003
引用本文: 中华医学会器官移植学分会. 常染色体显性遗传性多囊肾病肾移植临床技术操作规范(2022版)[J]. 器官移植, 2023, 14(1): 24-30. doi: 10.3969/j.issn.1674-7445.2023.01.003
Branch of Organ Transplantation of Chinese Medical Association. Clinical technical operation specification of kidney transplantation for autosomal dominant polycystic kidney disease (2022 edition)[J]. ORGAN TRANSPLANTATION, 2023, 14(1): 24-30. doi: 10.3969/j.issn.1674-7445.2023.01.003
Citation: Branch of Organ Transplantation of Chinese Medical Association. Clinical technical operation specification of kidney transplantation for autosomal dominant polycystic kidney disease (2022 edition)[J]. ORGAN TRANSPLANTATION, 2023, 14(1): 24-30. doi: 10.3969/j.issn.1674-7445.2023.01.003

常染色体显性遗传性多囊肾病肾移植临床技术操作规范(2022版)

doi: 10.3969/j.issn.1674-7445.2023.01.003
基金项目: 

国家自然科学基金 82070765

医学免疫学国家重点实验室开放课题 NKMI2020K05

蛋白质组学国家重点实验室开放课题 SKLPO202009

详细信息
  • 中图分类号: R617, R692

Clinical technical operation specification of kidney transplantation for autosomal dominant polycystic kidney disease (2022 edition)

  • 摘要: 常染色体显性遗传性多囊肾病(ADPKD)是最常见的遗传性肾病,也是终末期肾病(ESRD)的最常见原因之一。肾移植是ADPKD伴ESRD患者的最佳肾脏替代治疗方式,目前国内外学者对于ADPKD患者肾移植前多囊肾是否需要切除存在一定的争议,并且多囊肾切除手术标准及手术方式也不尽相同。为进一步规范ADPKD患者肾移植的临床技术操作,中华医学会器官移植学分会组织器官移植学专家从ADPKD的诊断、ADPKD肾移植的适应证和禁忌证、术前评估及处理、多囊肾切除术、术后管理等方面,制定本规范。

     

  • 图  1  多囊肾外科手术介入时机及手术方式推荐

    Figure  1.  The recommended timing of intervention and operation method in polycystic kidney surgery

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出版历程
  • 收稿日期:  2022-10-21
  • 网络出版日期:  2023-01-17
  • 刊出日期:  2023-01-15

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